Journal of Neuro-Oncology

, Volume 104, Issue 2, pp 599–604 | Cite as

Extraventricular anaplastic ependymoma with metastasis to scalp and neck

  • Matthew J. Davis
  • Fauzia Hasan
  • Ilan Weinreb
  • M. Christopher Wallace
  • Tim-Rasmus Kiehl
Case Report


We report a case of anaplastic ependymoma with extracranial metastases in a 22-year-old female. The patient originally presented with headaches and dysarthria. Neuroimaging revealed a large solid and cystic right fronto-temporal lesion. It was located completely extraventricularly and a glioblastoma was suspected based on the neuroimaging findings. A gross total resection was achieved. Histopathologic examination revealed an anaplastic ependymoma. The patient was treated with radiotherapy. Approximately 1 year after the initial surgery, the patient presented with metastatic disease to the scalp. At 2 years, an intraparotid metastasis was detected. Subsequent neck dissection revealed positive lymph nodes at several levels. It was followed by radiotherapy to the neck. 5 years after the initial surgery, the patient has residual metastatic disease. The case is discussed and the literature on extraventricular ependymal neoplasms is reviewed.


Anaplastic ependymoma Metastasis Scalp Neck 


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Copyright information

© Springer Science+Business Media, LLC. 2011

Authors and Affiliations

  • Matthew J. Davis
    • 1
  • Fauzia Hasan
    • 3
  • Ilan Weinreb
    • 2
    • 3
  • M. Christopher Wallace
    • 4
    • 5
  • Tim-Rasmus Kiehl
    • 2
    • 3
  1. 1.The Ruth and Bruce Rappaport Faculty of Medicine Technion - Israel Institute of TechnologyHaifaIsrael
  2. 2.Department of PathologyUniversity Health NetworkTorontoCanada
  3. 3.Department of Laboratory Medicine and PathobiologyUniversity of TorontoTorontoCanada
  4. 4.The Krembil Neuroscience CentreUniversity Health NetworkTorontoCanada
  5. 5.Division of Neurosurgery, Department of SurgeryUniversity of TorontoTorontoCanada

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