Accuracy of Body Size Estimation in Youth with Cystic Fibrosis and Association with Health-Related Quality of Life

  • Stacey L. SimonEmail author
  • Kaitlyn A. Ferris
  • Kristine Durkin
  • Kristin Riekert
  • Christina Duncan


Accuracy of body size estimation may impact motivation to adhere to treatment recommendations and health-related quality of life (HRQOL) in youth with cystic fibrosis (CF), but this has not yet been investigated. Thus, the goal of the current study was to examine accuracy of body size estimation in youth with CF, and associations with HRQOL, lung functioning, and dietary intake. Fifty-four youth diagnosed with CF (M = 13.61 years) completed the Figure Rating Scale, the Cystic Fibrosis QuestionnaireRevised, and a 24-h diet recall interview. Cohen’s Weighted Kappa Coefficient evaluated agreement between body size estimation and BMI percentile. Binary logistic regression analyses examined associations between body size accuracy and HRQOL, lung functioning, and dietary intake. A less than adequate agreement was found between youth body size estimation and BMI percentile. Most participants overestimated body size (69.8%). Body Image HRQOL, but neither lung functioning nor dietary intake, was significantly associated with body size estimation accuracy. Working with patients to improve perceptions of body size may also improve HRQOL scores and allow for discussion about treatment goals related to body size.


Cystic fibrosis Adolescents Body image Nutrition Adherence 



This work was supported by the Center for Pediatric Psychology and Family Studies at the University of Florida and The Blue Foundation for a Healthy Florida.

Compliance with Ethical Standards

Conflict of interest

Stacey L. Simon, Kaitlyn A. Ferris, Kristine Durkin, Kristin Riekert, and Christina Duncan declare that they have no conflict of interest.

Ethical Approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional review board and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

Human and Animal Rights

This article does not contain any studies with animals performed by any of the authors.

Informed Consent

Informed consent and child assent was obtained from all individual participants included in the study.


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© Springer Science+Business Media, LLC, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Department of Pediatrics, Division of Pulmonary MedicineUniversity of Colorado Anschutz Medical Campus, and Children’s Hospital ColoradoAuroraUSA
  2. 2.Outlier Research & EvaluationUChicago STEM Education, University of ChicagoChicagoUSA
  3. 3.Department of PsychologyWest Virginia UniversityMorgantownUSA
  4. 4.Division of Pulmonary & Critical Care Medicine, Department of MedicineJohns Hopkins UniversityBaltimoreUSA

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