Immune Dysregulation Syndromes (IPEX, CD27 Deficiency, and Others): Always Doomed from the Start?
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KeywordsAutoimmune Hepatitis Allogeneic Hematopoietic Stem Cell Transplantation Treg Function CD27 Deficiency Intractable Diarrhea
B. Prietl, A. Raicht, and the laboratory teams of T. Pieber and W. Schwinger, Medical University Graz, are thanked for performing immune phenotypical and functional analyses and for their helpful cooperation.
MGS compiled the clinical data of the patients, designed the study, and wrote the manuscript, OAH and KB generated and analyzed laboratory data and edited the final draft.
Compliance with Ethical Standards
MGS was in part funded by a grant from “Steirische Kinderkrebshilfe” (grant number A27213004019).
Conflict of Interest
The authors declare no conflict of interest in relation to this manuscript.
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