Catheter ablation of ventricular tachycardia in arrhythmogenic right ventricular dysplasia

  • Mauricio Arruda
  • Luciana Armaganijan
  • Tamer Fahmy
  • Luigi Di Biase
  • Dimpi Patel
  • Andrea Natale
Article

Abstract

Arrhythmogenic right ventricular dysplasia (ARVD) is a progressive, genetically determined fibro-fatty infiltrative myocardial disease with an estimated prevalence in the general population to be 1:5,000 to 1:10,000. ARVD leads to electrical instability that may predispose to life-threatening ventricular arrhythmia, heart failure, and sudden death. We reviewed the pathological substrate for ventricular arrhythmias, ECG findings and treatment modalities in ARVD. Importantly, novel techniques such as electroanatomic and voltage mapping has greatly improved the identification of the scared substrate in the settings of ARVD and have improved safety and efficacy of VT ablation procedures associated with this entity.

Keywords

Catheter ablation Arrhythmogenic right ventricular dysplasia ARVD Ablation in arrhythmogenic right ventricular dysplasia 

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Copyright information

© Springer Science+Business Media, LLC 2008

Authors and Affiliations

  • Mauricio Arruda
    • 1
  • Luciana Armaganijan
    • 3
  • Tamer Fahmy
    • 4
  • Luigi Di Biase
    • 2
  • Dimpi Patel
    • 2
  • Andrea Natale
    • 2
  1. 1.Electrophysiology SectionUniversity Hospitals Harrington-McLaughlin Heart and Vascular Institute, Case Western Reserve University School of MedicineClevelandUSA
  2. 2.Texas Cardiac Arrhythmias InstituteAustinUSA
  3. 3.Hamilton Health SciencesHamiltonCanada
  4. 4.Department of Critical Care MedicineCairo UniversityCairoEgypt

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