Posterior lenticonus is a rare progressive disease characterized by protrusion of posterior lens capsule along with lens cortex into the vitreous cavity. It may be associated with local thinning or absence of posterior lens capsule. It generally occurs sporadically, but familial cases have also been reported. If visually significant or if amblyopia is present, lens removal is indicated. Treatment consists of clear or cataractous lens extraction, optical correction along with prompt amblyopia therapy. In this case, we propose a “jellyfish sign” seen intraoperatively, which is referred to the characteristic movement of the posterior capsular cataractous material on injection of balanced salt solution in the capsular bag.
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