International Ophthalmology

, Volume 34, Issue 5, pp 1137–1140 | Cite as

Primary Ewing’s sarcoma of the orbit with intracranial extension abutting the temporal lobe: a rare case report

  • Syed Hassan Abbas NaqviEmail author
  • Saad Hameed
  • Syed Hassan Shiraz Naqvi
  • Muhammad Anis Musani
Case Report


Ewing’s sarcoma is a small, blue, round-cell tumor of mesenchymal origin which typically presents itself during the first and the second decades of life. Typically, it is noticed in the long bones of the limbs, pelvis, or ribs. There have been few reports worldwide with none in Pakistan of this rare phenomenon. We report here the case of a 16-year-old female diagnosed with Ewing’s sarcoma with intracranial extension abutting the temporal lobe resulting in proptosis and partial loss of vision in the left eye. The purpose of this case is to discuss the clinicoradiological presentation, microscopic description, and management of the patient.


Ewing’s sarcoma Intracranial Diagnosis Management 



The authors like to thank the patient for providing consent to publish this case. We also appreciate the Radiology Department of Jinnah Postgraduate Medical Center and Agha Khan Hospital for providing the images necessary to complete this report. We also thank Muhammad Yasin Bandukda who assisted in editing this manuscript.

Conflict of interest

All authors declare that no competing interests exist.


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Copyright information

© Springer Science+Business Media Dordrecht 2014

Authors and Affiliations

  • Syed Hassan Abbas Naqvi
    • 1
    • 3
    Email author
  • Saad Hameed
    • 2
  • Syed Hassan Shiraz Naqvi
    • 1
  • Muhammad Anis Musani
    • 2
  1. 1.Dow Medical CollegeDow University of Health SciencesKarachiPakistan
  2. 2.Sindh Medical CollegeDow University of Health SciencesKarachiPakistan
  3. 3.KarachiPakistan

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