Cardiac resynchronization and implantable defibrillators in adults with congenital heart disease

  • Henry ChubbEmail author
  • Kara S. Motonaga


Cardiac resynchronization therapy (CRT) and implantable cardioverter defibrillators (ICDs) are well-established therapies for adult patients with heart failure that have been shown to improve morbidity and mortality. However, the benefits and indications for use in adults with congenital heart disease (ACHD) are less defined with no significant large prospective studies in this population. There are, however, multiple retrospective studies that demonstrate the efficacy of these devices in the ACHD population. These indicate a role for both CRT and ICDs in select patients with ACHD. The clinician and patient must balance the risks and benefits, summarized in complex evidence that reflects the heterogeneity of the ACHD patient group, and apply them in a patient-specific manner to optimize the utility of CRT and ICDs.


Congenital heart disease Heart failure Dyssynchrony Sudden cardiac death Cardiac resynchronization therapy Implantable cardioverter defibrillator 


Compliance with ethical standards

Conflict of interest

Henry Chubb: No disclosures

Kara Motonaga: Medtronic and Abbott: Educational support


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© Springer Science+Business Media, LLC, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Division of Pediatric Cardiology, Department of PediatricsStanford UniversityPalo AltoUSA
  2. 2.Division of Pediatric Cardiothoracic Surgery, Department of Cardiothoracic SurgeryStanford UniversityPalo AltoUSA
  3. 3.Heart Center Research CoreStanford UniversityPalo AltoUSA

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