Documenta Ophthalmologica

, Volume 116, Issue 2, pp 91–95 | Cite as

Annular fundus autofluorescence abnormality in a case of macular dystrophy

  • Charlotte M. PoloschekEmail author
  • Lutz L. Hansen
  • Michael Bach
Original Research Article


Purpose: To present a case of macular dystrophy with early changes in fundus autofluorescence. Methods: A 20-year-old woman with a recent loss of visual acuity and onset of photophobia was examined. Color vision and visual field testing, fluorescein angiography, full-field and multifocal electroretinograms as well as fundus autofluorescence were performed. Results: Best-corrected visual acuity was 20/100 (right eye) and 20/60 (left eye). There was a red-green color vision defect and a relative central scotoma in both eyes. Ophthalmoscopy and fluorescein angiography were essentially normal, the presence of a dark choroid was debatable. Full-field ERG responses were normal, but the multifocal ERG showed severely reduced responses in the macular region. Both eyes showed a slight circular parafoveolar increase of fundus autofluorescence. Conclusion: Besides multifocal ERG, fundus autofluorescence aids to objectively assess the manifestation of macular dystrophies but does not discern between different types in early stages.


Fundus autofluorescence Central cone dystrophy Full-field electroretinogram Hereditary retinal dystrophy Macular dystrophy Occult macular dystrophy Multifocal electroretinogram Stargardt macular dystrophy-fundus flavimaculatus 


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Copyright information

© Springer-Verlag 2007

Authors and Affiliations

  • Charlotte M. Poloschek
    • 1
    Email author
  • Lutz L. Hansen
    • 1
  • Michael Bach
    • 1
  1. 1.Department of OphthalmologyUniversity of FreiburgFreiburgGermany

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