Advertisement

Dynamic outflow tract obstruction in congenitally corrected transposition of the great arteries

  • 88 Accesses

  • 4 Citations

Abstract

Congenitally corrected transposition of the great arteries (CCTGA) is a rare form of congenital heart disease, constituting 0.5% of all congenital heart defects. The incidence of left ventricle (non-systemic ventricle) outflow tract obstruction ranges between 44 and 57%. Herein, we present the case of a 45 year old woman with CCTGA with progressively worsening dyspnea who had been referred for surgical correction of severe systemic ventricle (morphologic right ventricle) atrio-ventricular valve (tricuspid valve) regurgitation. Cardiac magnetic resonance imaging (CMR) and transesophageal imaging (TEE) demonstrated severe systemic ventricle (morphologic right ventricle) contractile dysfunction, as well as dynamic non-systemic ventricle (morphologic left ventricle) outflow tract obstruction due to systolic anterior motion (SAM) of the non-systemic ventricle (morphologic left ventricle) atrio-ventricular valve (mitral valve) with a large membranous ventricular septal aneurysm that protrudes into the outflow tract of the non-systemic ventricle (morphologic left ventricle). Ultimately, our patient was felt to be too high-risk for surgical correction and a course of medical therapy has been pursued.

This is a preview of subscription content, log in to check access.

Access options

Buy single article

Instant unlimited access to the full article PDF.

US$ 39.95

Price includes VAT for USA

Subscribe to journal

Immediate online access to all issues from 2019. Subscription will auto renew annually.

US$ 99

This is the net price. Taxes to be calculated in checkout.

Fig. 1

References

  1. 1.

    Warnes CA (2006) Transposition of the great arteries. Circulation 114:2699–2709

  2. 2.

    Caso P, Ascione L, Lange A, Palka P, Mininni N, Sutherland GR (1998) Diagnostic value of transesophageal echocardiography in the assessment of congenitally corrected transposition of the great arteries in adult patients. Am Heart J 135:43–50

  3. 3.

    Reddy SC, Chopra PS, Rao PS (1997) Aneurysm of the membranous ventricular septum resulting in pulmonary outflow tract obstruction in congenitally corrected transposition of the great arteries. Am Heart J 133:112–119

Download references

Author information

Correspondence to Venu Menon.

Electronic supplementary material

Below is the link to the electronic supplementary material.

Supplementary material 2 (AVI 14729 kb)

Supplementary material 3 (AVI 12961 kb)

Supplementary material 1 (AVI 1351 kb)

Supplementary material 2 (AVI 14729 kb)

Supplementary material 3 (AVI 12961 kb)

Rights and permissions

Reprints and Permissions

About this article

Cite this article

Zurick III, A.O., Menon, V. Dynamic outflow tract obstruction in congenitally corrected transposition of the great arteries. Int J Cardiovasc Imaging 26, 617–619 (2010). https://doi.org/10.1007/s10554-010-9588-1

Download citation

Keywords

  • Congenital heart disease
  • Echocardiography
  • Cardiac magnetic resonance imaging