Evaluation and course of an unusual case of arrhythmogenic right ventricular dysplasia

  • Jan Fritz
  • Harikrishna Tandri
  • E. Rene Rodriguez
  • Hugh Calkins
  • David A. Bluemke
Case Report


We report a case of a 42-year-old Caucasian man who presented with isolated right ventricular failure and atrial fibrillation without ventricular arrhythmia. In this report, we describe accurate evaluation by MR imaging confirmed by histopathologic findings as well as imaging progression of this unusual case of arrhythmogenic right ventricular dysplasia.

Key words

arrhythmogenic right ventricular dysplasia arrhythmogenic right ventricular cardiomyopathy magnetic resonance imaging right ventricle 


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  1. 1.
    1. Marcus FI, Fontaine G. (1995). Arrhythmogenic right ventricular dysplasia/cardiomyopathy: a review. Pacing Clin Electrophysiol 18(6):1298–314PubMedCrossRefGoogle Scholar
  2. 2.
    2. Corrado D, Basso C, Thiene G, McKenna WJ, Davies MJ, Fontaliran F et al. (1997). Spectrum of clinicopathologic manifestations of arrhythmogenic right ventricular cardiomyopathy/dysplasia: a multicenter study. J Am Coll Cardiol 30(6):1512–20PubMedCrossRefGoogle Scholar
  3. 3.
    3. Blake LM, Scheinman MM, Higgins CB. (1994). MR features of arrhythmogenic right ventricular dysplasia. AJR Am J Roentgenol 162(4):809–12Google Scholar
  4. 4.
    4. Molinari G, Sardanelli F, Zandrino F, Parodi RC, Bertero G, Richiardi E et al. (2000). Adipose replacement and wall motion abnormalities in right ventricle arrhythmias: evaluation by MR imaging. Retrospective evaluation on 124 patients. Int J Card Imaging 16(2):105–15CrossRefGoogle Scholar
  5. 5.
    5. Bluemke DA, Krupinski EA, Ovitt T, Gear K, Unger E, Axel L et al. (2003). MR Imaging of arrhythmogenic right ventricular cardiomyopathy: morphologic findings and interobserver reliability. Cardiology 99(3):153–62PubMedCrossRefGoogle Scholar
  6. 6.
    6. Midiri M, Finazzo M. (2001). MR imaging of arrhythmogenic right ventricular dysplasia. Int J Cardiovasc Imaging 17(4):297–304CrossRefGoogle Scholar
  7. 7.
    7. Wagner A, Mahrholdt H, Sechtem U, Kim RJ, Judd RM. (2003). MR imaging of myocardial perfusion and viability. Magn Reson Imaging Clin N Am 11(1):49–66CrossRefGoogle Scholar
  8. 8.
    8. Gregoratos G, Abrams J, Epstein AE, Freedman RA, Hayes DL, Hlatky MA et al. (2002). ACC/AHA/NASPE 2002 guideline update for implantation of cardiac pacemakers and antiarrhythmia devices: summary article. A report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (ACC/AHA/NASPE Committee to Update the 1998 Pacemaker Guidelines). J Cardiovasc Electrophysiol 13(11):1183–99CrossRefPubMedGoogle Scholar
  9. 9.
    9. McKenna WJ, Thiene G, Nava A, Fontaliran F, Blomstrom-Lundqvist C, Fontaine G et al. (1994). Diagnosis of arrhythmogenic right ventricular dysplasia/cardiomyopathy. Task Force of the Working Group Myocardial and Pericardial Disease of the European Society of Cardiology and of the Scientific Council on Cardiomyopathies of the International Society and Federation of Cardiology. Br Heart J 71(3):215–8PubMedCrossRefGoogle Scholar
  10. 10.
    10. Corrado D, Basso C, Thiene G. (2000). Arrhythmogenic right ventricular cardiomyopathy: diagnosis, prognosis, and treatment. Heart 83(5):588–95CrossRefPubMedGoogle Scholar
  11. 11.
    11. van der Wall EE, Kayser HW, Bootsma MM, de Roos A, Schalij MJ. (2000). Arrhythmogenic right ventricular dysplasia: MRI findings. Herz 25(4):356–64PubMedCrossRefGoogle Scholar
  12. 12.
    12. Kayser HW, de RA, van der Wall EE. (1998). Diagnosis of cardiac abnormalities in patients with nonischemic tachyarrhythmias: additional value of MR imaging. Int J Card Imaging 14(4):279–85CrossRefGoogle Scholar
  13. 13.
    13. Tandri H, Rutberg J, Bluemke DA, Calkins H. (2002). Magnetic resonance imaging of arrhythmogenic right ventricular dysplasia. J Cardiovasc Electrophysiol 13(11):1180CrossRefPubMedGoogle Scholar
  14. 14.
    14. Tandri H, Saranathan M, Rodriguez ER, Martinez C, Bomma C, Nasir K et al. (2005). Noninvasive detection of myocardial fibrosis in arrhythmogenic right ventricular cardiomyopathy using delayed-enhancement magnetic resonance imaging. J Am Coll Cardiol 45(1):98–103CrossRefPubMedGoogle Scholar
  15. 15.
    15. Keller DI, Osswald S, Bremerich J, Bongartz G, Cron TA, Hilti P et al. (2003). Arrhythmogenic right ventricular cardiomyopathy: diagnostic and prognostic value of the cardiac MRI in relation to arrhythmia-free survival. Int J Cardiovasc Imaging 19(6):537–43CrossRefGoogle Scholar

Copyright information

© Springer Science+Business Media, Inc. 2005

Authors and Affiliations

  • Jan Fritz
    • 1
  • Harikrishna Tandri
    • 1
  • E. Rene Rodriguez
    • 1
  • Hugh Calkins
    • 1
  • David A. Bluemke
    • 1
  1. 1.Russell H. Morgan Department of Radiology and Radiological ScienceJohns Hopkins University School of MedicineBaltimoreUSA
  2. 2.Russell H. Morgan Department of Radiology and Radiological ScienceJohns Hopkins University School of MedicineBaltimoreUSA

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