Agenesis of the dorsal pancreas: a very rare entity causing diabetes mellitus

  • Patrick DinkhauserEmail author
  • Johannes Paesold
  • Dietmar Hubner
  • Verena Steffan
  • Ronald Lampl
  • Harald Hofer
case report


Dorsal pancreatic agenesis is a very rare pancreatic developmental anomaly resulting in missing corpus and cauda of the pancreas. Due to improvements and more widespread use of advanced radiological techniques like CT or MRI, the possibility of finding this disorder is growing. Thus, this rare congenital condition, as well as a pancreas divisum and pseudo-agenesis secondary to chronic pancreatitis, must be considered in the differential diagnosis. Although most of the patients seem to be asymptomatic, abdominal pain and pancreatitis may develop. Moreover, this entity should be known by the treating physician, as these patients are at a high risk of developing diabetes mellitus during their lifetime. Herein, we present the case of a 65-year-old woman with complete agenesis of the dorsal pancreas. The patient was hospitalized due to weight loss, abdominal discomfort, and diabetes mellitus type 2.


Pancreatic anomaly Fetal pancreatic development Exocrine pancreatic insufficiency Weight loss Pancreatitis 


Conflict of interest

P. Dinkhauser, J. Paesold, D. Hubner, V. Steffan, R. Lampl, and H. Hofer declare that they have no competing interests.


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Copyright information

© Springer-Verlag GmbH Austria, ein Teil von Springer Nature 2019

Authors and Affiliations

  1. 1.Department of Internal Medicine I, Division of Gastroenterology and Hepatology, Endocrinology and RheumatologyKlinikum Wels-GrieskirchenWelsAustria
  2. 2.Department of RadiologyKlinikum Wels-GrieskirchenWelsAustria

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