Zeitschrift für Epileptologie

, Volume 23, Issue 4, pp 244–248 | Cite as

Jeavons-Syndrom

  • T. Cloppenborg
  • G. Classen
  • E. Korn-Merker
  • T. Polster
  • A. Ebner
Originalarbeit
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Zusammenfassung

Das Syndrom der Augenlidmyoklonien mit Absencen (Jeavons-Syndrom) ist durch augenschlussinduzierte Lidmyoklonien mit oder ohne Absencen, begleitende generalisierte EEG-Paroxysmen und Fotosensibilität charakterisiert. Schwierigkeiten in der Diagnosefindung bereiten die Abgrenzung einfacher Lidmyoklonien als Anfallsform bei idiopathisch generalisierten Epilepsien und eine veränderte Fotosensitivität unter antikonvulsiver Medikation. Es werden anhand zweier klinischer Beispiele die typischen Befunde des Jeavons-Syndroms dargestellt und differenzialdiagnostische Schwierigkeiten aufgezeigt.

Schlüsselwörter

Augenlider Myoklonus Lidschlussinduktion Differenzialdiagnose Epilepsie 

Jeavons syndrome

Abstract

Eyelid myoclonia with absences (Jeavons syndrome) is characterized by eye closure-induced eyelid myoclonias with or without absences, generalized EEG paroxysms, and photosensitivity. Simple eyelid myoclonias as seizure semiology in other idiopathic generalized epilepsies and the loss of photosensitivity under antiepileptic medication complicate the diagnosis. The history and clinical features of two patients with Jeavons syndrome are described and difficulties with the differential diagnosis are discussed.

Keywords

Eyelids Myoclonus Lid closure, induction Diagnosis, differential Epilepsy 
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Notes

Danksagung

Ein besonderer Dank gilt unseren Kolleginnen und Kollegen aus dem Epilepsiezentrum Bethel, insbesondere Frau Stutterheim, Herrn Specht, Herrn Schoendienst und Herrn Woermann.

Interessenkonflikt

Die Autoren geben an, dass kein Interessenkonflikt besteht.

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Copyright information

© Springer 2010

Authors and Affiliations

  • T. Cloppenborg
    • 1
  • G. Classen
    • 1
  • E. Korn-Merker
    • 1
  • T. Polster
    • 1
  • A. Ebner
    • 1
  1. 1.Epilepsiezentrum Bethel/Klinik MaraBielefeldDeutschland

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