IgG4-related disease involving the sclera

  • Kyotaro Ohno
  • Yasuharu Sato
  • Koh-ichi Ohshima
  • Katsuyoshi Takata
  • Midori Ando
  • Lamia Abd Al-Kader
  • Noriko Iwaki
  • Mai Takeuchi
  • Yorihisa Orita
  • Tadashi Yoshino
Case Report

Abstract

A 49-year-old female patient previously treated for scleritis and uveitis-induced cataract in the right eye presented with a subretinal white lesion in the same eye. With a preliminary diagnosis of choroidal tumor, enucleation of the eyeball was performed in accordance with the patient’s request. Histologic and immunohistologic examinations were consistent with immunoglobulin G4-related disease. The case demonstrates that it is important to consider IgG4-related disease in the differential diagnosis of an intraocular tumor.

Keywords

IgG4-related disease Eyeball Sclera 

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Copyright information

© Japan College of Rheumatology 2012

Authors and Affiliations

  • Kyotaro Ohno
    • 1
  • Yasuharu Sato
    • 1
  • Koh-ichi Ohshima
    • 2
  • Katsuyoshi Takata
    • 1
  • Midori Ando
    • 1
  • Lamia Abd Al-Kader
    • 1
    • 3
  • Noriko Iwaki
    • 1
  • Mai Takeuchi
    • 1
  • Yorihisa Orita
    • 4
  • Tadashi Yoshino
    • 1
  1. 1.Department of PathologyOkayama University Graduate School of Medicine, Dentistry, and Pharmaceutical ScienceKita-ku, OkayamaJapan
  2. 2.Department of OphthalmologyNational Hospital Organization Okayama Medical CenterOkayamaJapan
  3. 3.Department of Pathology, Faculty of MedicineMansoura UniversityMansouraEgypt
  4. 4.Department of Otolaryngology, Head and Neck SurgeryOkayama University Graduate School of Medicine, Dentistry, and Pharmaceutical ScienceKita-ku, OkayamaJapan

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