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Neurosurgical Review

, Volume 28, Issue 4, pp 320–325 | Cite as

Dorsal intramedullary dermoids

  • Marwan W. Najjar
  • John A. Kusske
  • Anton N. Hasso
Case Report

Abstract

We report a case of a 31-year-old woman with an intramedullary thoracic dermoid, who had progressive spastic paraparesis in her lower extremities over a period of three years, as well as loss of bowel and bladder control. She had been operated for “spina bifida” at three days of age but had no neurologic deficit. MRI of the thoracic spine showed an intramedullary hypointense lesion at T7–T8, associated with an intramedullary lipoma at a higher level. Intracapsular resection of an intramedullary dermoid cyst was performed. We review the literature on intramedullary dermoids differentiating them from the more common, but still rare, lumbosacral subdural juxtamedullary dermoids. We discuss the associated malformations with these lesions, as well as their pathophysiology and treatment. Although uncommon, dorsal intramedullary dermoids should be suspected and treated in a timely manner, especially in presence of other congenital anomalies.

Keywords

Intramedullary dermoid Dermal sinus Congenital spinal malformation Spinal cord tumor 

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Copyright information

© Springer-Verlag 2005

Authors and Affiliations

  • Marwan W. Najjar
    • 1
    • 2
  • John A. Kusske
    • 3
  • Anton N. Hasso
    • 4
  1. 1.Dr. Erfan and Bagedo HospitalsJeddahSaudi Arabia
  2. 2.Department of SurgeryAmerican University of BeirutBeirutLebanon
  3. 3.Department of Neurological SurgeryUniversity of CaliforniaIrvineUSA
  4. 4.University of CaliforniaIrvineUSA

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