Dyke-Davidoff-Masson syndrome: an unusual case of late diagnosis
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Dyke-Davidoff-Masson syndrome (DDMS) is a rare neurological disorder usually observed during childhood and classically characterized by epilepsy, hemiparesia/hemiplegia, facial asymmetry, and mental retardation. It is radiologically characterized by partial or diffuse cerebral hemiatrophy [1, 2].
DDMS can be classified as congenital when it occurs before 2 years of age, typically resulting from intrauterine or neonatal vascular insults, whereas the acquired form can arise due to a variety of brain insults, including asphyxia, traumas, infections, prolonged febrile seizures, ischemia, and brain hemorrhages. The onset and presentation are variable . It is our intention to expose an unusual case in which diffuse cerebral hemiatrophy occurred mid-life, accompanying a previous history of mild neurological symptoms. We explore the clinical features and radiological findings and propose an unusual evolution and late diagnosis of acquired DDMS.
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