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Juvenile polymyositis associated with ureteral necrosis: a diagnostic and therapeutic dilemma—case report and review of the literature

  • Ruby HavivEmail author
  • Tania Zehavi
  • Avishalom Pomeranz
  • Ilan Leibovitch
  • Amos Neheman
  • Yosef Uziel
Case Based Review
  • 2 Downloads

Abstract

We describe an 11-year-old girl, diagnosed with juvenile polymyositis (JPM), who developed right ureteral obstruction secondary to necrosis. We emphasize the dilemmas regarding optimal timing for surgical intervention and medical treatment. Vascular involvement, which could be a part of juvenile dermatomyositis, may also be a feature of JPM. We discuss the association between vasculopathy and ureteral necrosis and review the literature regarding similar conditions. Whether the ureteral necrosis is a specific feature of vasculopathy, or a result of visceral calcinosis, needs to be further explored.

Keywords

Calcinosis JDM JPM Juvenile dermatomyositis Necrosis Polymyositis Stenosis Ureter Vasculopathy 

Notes

Acknowledgments

We thank Faye Schreiber, MS for editing the manuscript.

Compliance with ethical standards

Ethical standards

This study was performed in accordance with the ethical standards laid down in the 1964 Declaration of Helsinki and its later amendments.

The patient’s parents provided informed consent to publish their daughter’s case anonymously.

Disclosures

None

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Copyright information

© International League of Associations for Rheumatology (ILAR) 2019

Authors and Affiliations

  1. 1.Pediatric Rheumatology Unit, Department of PediatricsMeir Medical CenterKfar SabaIsrael
  2. 2.Sackler Faculty of MedicineTel Aviv UniversityTel AvivIsrael
  3. 3.Pathology DepartmentMeir Medical CenterKfar SabaIsrael
  4. 4.Pediatric Nephrology UnitMeir Medical CenterKfar SabaIsrael
  5. 5.Department of UrologyMeir Medical CenterKfar SabaIsrael
  6. 6.Pediatric Urology UnitAssaf Harofeh Medical CenterBe’er Ya’akovIsrael

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