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Clinical Rheumatology

, Volume 26, Issue 11, pp 1993–1996 | Cite as

Hughes–Stovin syndrome: is it incomplete Behçet’s?

Report of two cases and review of the literature
  • Yasser Emad
  • Yasser Ragab
  • Abd El-Hakim Shawki
  • Tamer Gheita
  • Ahmed El-Marakbi
  • Mohamed Hanfi Salama
Case Report

Abstract

In this report, we described two male patients with Hughes–Stovin syndrome. The first patient was a 26-year-old male who initially presented with deep vein thrombosis (DVT) in the right lower limb followed shortly by hemoptysis. Pulmonary CT angiography revealed bilateral pulmonary artery aneurysms secondary to underlying pulmonary vasculitis. While the second case was a 16-year-old male patient who initially presented with generalized fits due to sagittal sinus thrombosis and later followed by DVT in the left lower limb. Pulmonary CT angiography showed small pulmonary artery aneurysms with thrombosis of peripheral pulmonary artery branches. Both patients were treated successfully with steroids and immunosuppressive therapy and showed clinical improvement.

Keywords

Behcet’s disease Hughes–Stovin syndrome Incomplete Behcet’s disease Pulmonary vasculitis 

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Copyright information

© Clinical Rheumatology 2007

Authors and Affiliations

  • Yasser Emad
    • 1
    • 2
  • Yasser Ragab
    • 3
    • 4
  • Abd El-Hakim Shawki
    • 5
  • Tamer Gheita
    • 1
  • Ahmed El-Marakbi
    • 6
    • 7
  • Mohamed Hanfi Salama
    • 8
  1. 1.Rheumatology and Rehabilitation Department, Faculty of MedicineCairo UniversityCairoEgypt
  2. 2.Rheumatology and Rehabilitation DepartmentDr. Erfan and Bagedo HospitalJeddahSaudi Arabia
  3. 3.Radio Diagnosis Department, Faculty of MedicineCairo UniversityCairoEgypt
  4. 4.Radio Diagnosis DepartmentDr. Erfan and Bagedo HospitalJeddahSaudi Arabia
  5. 5.Neurology DepartmentDr. Erfan and Bagedo HospitalJeddahSaudi Arabia
  6. 6.General Surgery Department, Faculty of MedicineCairo UniversityCairoEgypt
  7. 7.Vascular UnitDr. Erfan and Bagedo HospitalJeddahSaudi Arabia
  8. 8.Rheumatology Department, Faculty of MedicineEl Azhar UniversityCairoEgypt

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