Clinical Rheumatology

, Volume 26, Issue 10, pp 1779–1781

Orofacial dystonia related to Sjogren’s syndrome

  • Sokratis G. Papageorgiou
  • Theodoros Kontaxis
  • Anastasios Bonakis
  • Nikolaos Kalfakis
Case Report

Abstract

Sjogren’s syndrome (SS), either primary or secondary, is rarely accompanied by CNS complications. We report the exceptional case of a patient with secondary SS, who presented orofacial dystonia as a consequence of her disease. Initial treatment with clonazepam and levetiracetam was unsuccessful. However, dystonia was dramatically improved by a treatment with corticosteroids. This case demonstrates that corticosteroids can be efficacious in the treatment of dystonia related to SS.

Keywords

Dystonia Orofacial dystonia Sjogren’s syndrome 

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Copyright information

© Clinical Rheumatology 2007

Authors and Affiliations

  • Sokratis G. Papageorgiou
    • 1
  • Theodoros Kontaxis
    • 1
  • Anastasios Bonakis
    • 1
  • Nikolaos Kalfakis
    • 1
  1. 1.Department of Neurology, Eginition Hospital, Medical SchoolUniversity of AthensAthensGreece

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