Pediatric and Developmental Pathology

, Volume 3, Issue 3, pp 271–276 | Cite as

Congenital Misalignment of Pulmonary Veins with Alveolar Capillary Dysplasia Causing Persistent Neonatal Pulmonary Hypertension: Report of Two Affected Siblings

  • Carmen Gutierrez
  • Angeles Rodriguez
  • Sylvia Palenzuela
  • Carolina Forteza
  • Jose L. Diaz Rossello
Article

Abstract

Misalignment of pulmonary vessels with alveolar capillary dysplasia is a rare cause of persistent pulmonary hypertension of the newborn. Most of the reported cases have been sporadic. We present two consecutive affected siblings with this disorder. This is the fifth reported family occurrence of this condition. In addition to the pulmonary abnormality, one of our cases had duodenal atresia.

Key words: congenital alveolar capillary dysplasia, family occurrence, misalignment of the pulmonary vessels, persistent neonatal pulmonary hypertension 

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Copyright information

© Society for Pediatric Pathology 2000

Authors and Affiliations

  • Carmen Gutierrez
    • 1
  • Angeles Rodriguez
    • 1
  • Sylvia Palenzuela
    • 1
  • Carolina Forteza
    • 2
  • Jose L. Diaz Rossello
    • 2
  1. 1.Pediatric Pathology Laboratory, Hospital Pereira Rossell, Boulevard Artigas 1550, Casilla de Correo 16059, MontevideoUruguay
  2. 2.Latin American Center for Perinatology and Human Development, Hospital de Clínicas, Avenida Italia s/n, CP 11600, MontevideoUruguay

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