Pediatric and Developmental Pathology

, Volume 8, Issue 6, pp 654–657

Zimmermann-Laband Syndrome in an Infant With an Atypical Histologic Finding

  • Mehmet Emre Atabek
  • Ozgur Pirgon
  • Ahmet Sert
  • Hatice Toy
Article

Abstract

Zimmermann-Laband syndrome is an inherited disorder that is characterized by abnormalities of the head, face, hands, and feet. Most children with this disorder have generalized hypertrichosis, large gingivae, and hypoplasia of the fingernails and toenails. We report a male infant who exhibited typical features of Zimmermann-Laband syndrome with an unusual histopathologic finding. Excised tissue from the infant’s gingivae showed papillary projections that were composed of hyperplastic stratified squamous epithelium with different amounts of keratinization.

Keywords

Zimmermann-Laband syndrome hypertrichosis gingival hyperplasia infant 

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Copyright information

© Society for Pediatric Pathology 2005

Authors and Affiliations

  • Mehmet Emre Atabek
    • 1
  • Ozgur Pirgon
    • 1
  • Ahmet Sert
    • 1
  • Hatice Toy
    • 2
  1. 1.Department of Pediatrics, Section of Pediatric Endocrinology, School of MedicineSelcuk UniversityKonya
  2. 2.Department of Pathology, School of MedicineSelcuk UniversityKonya

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