Pediatric and Developmental Pathology

, Volume 8, Issue 2, pp 240–244 | Cite as

Sudden, Unexpected Death Associated with Meningioangiomatosis: Case Report



We report a case of sudden, unexpected death associated with meningioangiomatosis in a 13-year-old, previously healthy male without a history of seizures, neurologic deficits, or clinical stigmata of neurofibromatosis. There was no family history of neurofibromatosis. The postmortem examination showed a 5-cm mass involving the right posterior frontal and orbital frontal cortex that had microscopic features diagnostic of meningioangiomatosis. Because no other cause of death was found, we postulate that he likely died as a result of a seizure secondary to meningioangiomatosis.


sudden unexpected death meningioangiomatosis seizure outcome 


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Copyright information

© Society for Pediatric Pathology 2005

Authors and Affiliations

  • Chris Wixom
    • 1
    • 2
  • Amy E. Chadwick
    • 1
  • Henry F. Krous
    • 1
    • 2
  1. 1.Children’s Hospital and Health CenterSan DiegoUSA
  2. 2.University of California at San Diego School of MedicineLa JollaUSA

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