Pediatric and Developmental Pathology

, Volume 8, Issue 1, pp 105–114 | Cite as

“Proximal-type” and Classic Epithelioid Sarcomas Represent a Clinicopathologic Continuum: Case Report

  • Dinesh Rakheja
  • Kathleen S. Wilson
  • John Meehan
  • Roger A. Schultz
  • Ana M. Gomez


We report a case of an epithelioid sarcoma that occurred in the right hand of a 14−year-old boy and had the “proximal-type” morphology and a complex, near-tetraploid karyotype. The tumor metastasized to the lungs, where the morphology was typical for the classic epithelioid sarcoma. Based on the morphologic and cytogenetic findings in this case, we suggest that the proximal-type and the classic epithelioid sarcomas are not distinct entities but represent a continuum.


epithelioid sarcoma proximal-type epithelioid sarcoma cytogenetics 


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Copyright information

© Society for Pediatric Pathology 2004

Authors and Affiliations

  • Dinesh Rakheja
    • 1
    • 2
  • Kathleen S. Wilson
    • 2
  • John Meehan
    • 3
  • Roger A. Schultz
    • 2
  • Ana M. Gomez
    • 1
    • 2
  1. 1.Department of PathologyChildren’s Medical Center of DallasDallasUSA
  2. 2.Department of PathologyUniversity of Texas Southwestern Medical CenterDallasUSA
  3. 3.Department of RadiologyChildren’s Medical Center of DallasDallasUSA

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