Pediatric and Developmental Pathology

, Volume 7, Issue 6, pp 653–660

Extrapleural Benign Solitary Fibrous Tumor in the Shoulder of a 9-Year-Old Girl: Case Report and Review of the Literature

  • Dinesh Rakheja
  • Kathleen S. Wilson
  • John J. Meehan
  • Roger A. Schultz
  • Gerhard E. Maale
  • Charles F. Timmons
Case report

Abstract

We report a case of a benign solitary fibrous tumor that occurred in the right shoulder of a 9-year-old girl. This case is remarkable due to the unusual location of its occurrence and the young age of the patient. In addition, cytogenetic analysis revealed a karyotype unreported in this neoplasm: 46,XX,der(4)t(4;9)(q31.1;q34), del(9)(p22p24),der(9)t(4;9)(q31.1;q34)ins(9;?)(q34;?) (17 cells)/46,XX (3 cells).

Keywords

extrapleural solitary fibrous tumor cytogenetics 

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Copyright information

© Springer Science+Business Media, Inc. 2004

Authors and Affiliations

  • Dinesh Rakheja
    • 1
    • 4
  • Kathleen S. Wilson
    • 1
  • John J. Meehan
    • 2
    • 4
  • Roger A. Schultz
    • 1
  • Gerhard E. Maale
    • 3
    • 4
  • Charles F. Timmons
    • 1
    • 4
  1. 1.Department of Pathology, MC 9073University of Texas Southwestern Medical CenterDallasUSA
  2. 2.Department of RadiologyUniversity of Texas Southwestern Medical CenterDallasUSA
  3. 3.Department of Orthopedic SurgeryUniversity of Texas Southwestern Medical CenterDallasUSA
  4. 4.Children’s Medical Center of DallasDallasUSA

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