Medical Molecular Morphology

, Volume 47, Issue 2, pp 68–75 | Cite as

Recent classification of renal epithelial tumors

Award Review


The recent classification of renal tumors is based on genetic evidence as well as on histologic features. Malignant tumor includes clear cell renal carcinoma (RCC), multilocular cystic RCC, papillary RCC, chromophobe RCC, carcinoma of the collecting duct of Bellini, renal carcinoma associated with Xp11.2 translocations/TFE3 gene fusions and mucinous tubular and spindle cell carcinoma. Benign tumor is subdivided into papillary adenoma, renal oncocytoma and metanephric adenoma. Recently, new disease entities such as acquired cystic disease-associated RCC, clear cell papillary RCC and renal carcinoma with t(6;11)(p21:q12) have been discovered. In this article, we briefly review and introduce the clinical, morphological and genetic features of these tumor entities.


Renal cell carcinoma WHO classification Renal cell carcinomas subtypes Pathology and genetics 


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Copyright information

© The Japanese Society for Clinical Molecular Morphology 2013

Authors and Affiliations

  1. 1.Department of PathologyKochi Red Cross HospitalKochi CityJapan

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