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Bipartite craniopharyngeal canal with a lipoma and cephalocele: a previously unreported entity

  • S. VinayagamaniEmail author
  • Bejoy Thomas
  • Jaypalsinh Gohil
  • Sabarish Sekar
  • Prakash Nair
  • Chandrasekharan Kesavadas
Case Report - Pediatric Neurosurgery
  • 9 Downloads
Part of the following topical collections:
  1. Pediatric Neurosurgery

Abstract

A 13-year-old male child was evaluated for headache and visual deterioration; he underwent routine MRI imaging which revealed a large craniopharyngeal canal, divided by an abnormal bony septum giving a bipartite appearance of the canal, with a lipoma and cephalocele on either side of the septum. The child had undergone a previous surgery for cleft palate repair at the age of 7. The child had normal pituitary function inspite of nonvisualization of pituitary gland in MRI. To best our knowledge, this is the first case with such a variation. We have also discussed the possible embryological hypothesis for this previously unreported entity. Knowledge about this rare variant might have surgical relevance in selected cases.

Keywords

Canal Bipartite Lipoma Cephalocele Postsphenoid center 

Abbreviations

CPC

Craniopharyngeal canal

MRI

Magnetic resonance imaging

CSF

Cerebrospinal fluid

CT

Computed tomography

FLAIR

Fluid attenuation inversion recovery

Notes

Authors’ contribution

S V: Manuscript writing, image analysis, manuscript editing

B T: Manuscript edition and critical revision

J G: Image analysis and description, manuscript edition

S S: Image analysis and description, manuscript edition

C K: Manuscript editing and critical revision

P N: Manuscript editing and critical revision

Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflict of interest.

Ethical approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

Patient consent

The patient’s guardian has consented to the submission of the case report for submission to the journal.

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Copyright information

© Springer-Verlag GmbH Austria, part of Springer Nature 2019

Authors and Affiliations

  1. 1.Department of Imaging Sciences and Interventional RadiologySree Chitra Tirunal Institute for Medical Sciences and TechnologyTrivandrumIndia
  2. 2.Department of NeurosurgerySree Chitra Tirunal Institute for Medical Sciences and TechnologyTrivandrumIndia

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