Meige syndrome (MS) is usually described as a combination of blepharospasm with oromandibular dystonia. There are a large number of case reports of deep brain stimulation (DBS) of the globus pallidus internus (GPI) for MS and only one report of unilateral pallidotomy (PT). We report the first case of staged bilateral PT for treatment of a patient with MS using intraoperative high-frequency stimulation in order to predict and prevent postoperative deficit. There was a significant improvement of the Burk-Fahn-Marsden dystonia rating scale from 26 to 3. There were no adverse postoperative neurological and neuropsychological events.
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Conflict of interest
The patient has consented to submission of this case report to the journal.
In this era of DBS hysteria, there are people who still believe in the benefit of non-expensive and well-performed stereotactic lesional procedures, and provide solid documentation about its benefit. This paper is one of them.
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Minkin, K., Gabrovski, K., Dimova, P. et al. Bilateral pallidotomy for Meige syndrome. Acta Neurochir 159, 1359–1363 (2017). https://doi.org/10.1007/s00701-017-3178-0
- Meige syndrome
- Deep brain stimulation
- Radiofrequency lesions
- High frequency stimulation