Acta Neurochirurgica

, Volume 155, Issue 7, pp 1229–1234

Primary extraosseous intradural spinal Ewing’s sarcoma: report of two cases

  • Giovanni Pancucci
  • Juan Antonio Simal-Julian
  • Estela Plaza-Ramirez
  • Raul García-Marcos
  • Empar Mayordomo-Aranda
  • Carlos Botella-Asunción
Case Report - Spine


Two cases of primary extraosseous intradural spinal Ewing’s sarcoma are reported with a review of the current literature. This rare neoplasm shares features with cerebral primitive neuroectodermal tumors, complicating a correct diagnosis. Gross total resection seems to be the main treatment, although adjuvant therapies could improve the prognosis. In case 1, a 56-year-old man presented with cauda equina syndrome. MRI showed an intradural tumor from L4 to S2. An emergency laminectomy was performed with gross total resection of a hemorrhagic tumor, followed by adjuvant treatment. In the second case, a 25-year-old female developed leg and lumbar pain. MRI study identified a homogeneously enhancing intradural mass at the L2-L3 level. A laminoplasty was performed, followed by tumor resection; no adjuvant treatment was administered afterwards. Immunohistochemical workup confirmed the diagnosis of Ewing’s sarcoma in both cases.


Ewing’s sarcoma Spinal cord neoplasms Intradural extramedullary Extracranial primitive neuroectodermal tumor 


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Copyright information

© Springer-Verlag Wien 2013

Authors and Affiliations

  • Giovanni Pancucci
    • 1
  • Juan Antonio Simal-Julian
    • 1
  • Estela Plaza-Ramirez
    • 1
  • Raul García-Marcos
    • 2
  • Empar Mayordomo-Aranda
    • 3
  • Carlos Botella-Asunción
    • 1
  1. 1.Department of Neurological SurgeryHospital Universitario La FeValenciaSpain
  2. 2.Department of RadiologyHospital Universitario La FeValenciaSpain
  3. 3.Department of PathologyHospital Universitario La FeValenciaSpain

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