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Acta Neurochirurgica

, Volume 153, Issue 7, pp 1511–1517 | Cite as

Atypical adult medulloblastoma

  • Maziar BehbahaniEmail author
  • Edward Jerome St. George
  • Laurance T. Dunn
  • Donald M. Hadley
  • William Stewart
Case Report

Abstract

Medulloblastomas are malignant primitive neuro-ectodermal neoplasms of childhood. In adults, clinical manifestations, imaging and prognosis can be different from that observed in children. Three adult patients with confirmed diagnoses of medulloblastoma are discussed in this report. They presented with unusually prolonged clinical courses and with imaging more suggestive of L’hermitte-Duclos disease. Medulloblastoma should be considered in all adults with posterior fossa masses despite having clinical and radiological features suggestive of a low-grade tumour. Definitive diagnosis requires histological confirmation in all cases.

Keywords

Medulloblastoma L’hermitte-Duclos disease Adult MRI characteristics 

Notes

Conflicts of interest

None.

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Copyright information

© Springer-Verlag 2011

Authors and Affiliations

  • Maziar Behbahani
    • 1
    Email author
  • Edward Jerome St. George
    • 1
  • Laurance T. Dunn
    • 1
  • Donald M. Hadley
    • 2
  • William Stewart
    • 3
  1. 1.Department of NeurosurgeryInstitute of Neurological Sciences, Southern General HospitalGlasgowUK
  2. 2.Department of NeuroradiologyInstitute of Neurological Sciences, Southern General HospitalGlasgowUK
  3. 3.Department of NeuropathologyInstitute of Neurological Sciences, Southern General HospitalGlasgowUK

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