Acta Neurochirurgica

, 151:1005 | Cite as

Extreme sensitivity of hearing to decreases of ICP in Menière’s disease

  • Arthur R. Kurzbuch
  • Armen Momjian
  • Keyvan Nicoucar
  • Shahan Momjian
Case Report


We report the case of a Menière’s disease patient affected by normal pressure hydrocephalus (NPH) who presented a cerebrospinal fluid (CSF) pressure-dependent hearing impairment after shunting. This side-effect was not only reversible and reproducible but occurred at a high opening pressure when the valve setting was lowered by only 0.7 mmHg (10 mmH2O). This observation suggests that hearing in Menière’s disease might be very sensitive to small reductions of intracranial pressure (ICP) and that these patients should be informed of this potential risk, which can compromise the efficacy of the shunt.


Hearing impairment Ventriculo-peritoneal shunt Normal pressure hydrocephalus CSF pressure Menière’s disease 


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Copyright information

© Springer-Verlag 2009

Authors and Affiliations

  • Arthur R. Kurzbuch
    • 1
  • Armen Momjian
    • 2
  • Keyvan Nicoucar
    • 3
  • Shahan Momjian
    • 1
  1. 1.Department of Clinical Neurosciences, Service of NeurosurgeryGeneva University Hospitals and University of GenevaGeneva 14Switzerland
  2. 2.Department of Surgery, Service of Maxillo-Facial and Oral SurgeryGeneva University Hospitals and University of GenevaGeneva 14Switzerland
  3. 3.Department of Clinical Neurosciences, Service of Otorhinolaryngology, Head and Neck SurgeryGeneva University Hospitals and University of GenevaGeneva 14Switzerland

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