Advertisement

Acta Neurochirurgica

, Volume 149, Issue 8, pp 829–830 | Cite as

Sturge-Weber syndrome accompanied with multiple congenital intracranial lesions

  • R. Ergün
  • A. İ. Ökten
  • Y. Gezercan
  • A. R. Gezici
Case Report

Summary

Sturge-Weber syndrome is one of the neurocutaneous syndromes. It is a rare, nonfamiliar disease that is characterized by facial port-wine stain, leptomeningeal angiomatosis, choroidal angioma, buphthalmos, intracranial calcification, cerebral atrophy, mental retardation, glaucoma, seizures and hemiparesis. CT and MR are complementary in the evaluation of this disease. Epilepsy is an essential feature of Sturge-Weber syndrome and it has a major significance for prognosis and treatment. We report a 2-year-old boy with Sturge-Weber syndrome who had in addition an intracranial lipoma, a temporal arachnoid cyst and a porencephalic cyst. This combination of intracranial lesions with Sturge-Weber syndrome has not been previously reported.

Keywords: Brain; calcification; epilepsy; Sturge-Weber syndrome 

References

  1. Akpinar, E 2004The tram-track sign: cortical calcificationsRadiology231515516PubMedCrossRefGoogle Scholar
  2. Arzimanoglou, A, Aicardi, J 1992The epilepsy of Sturge-Weber syndrome: clinical features and treatment in 23 patientsActa Neurol Scand (Suppl)1401822CrossRefGoogle Scholar
  3. Arzimanoglou, A, Andermann, F, Aicardi, J, Sainte-Rose, C, Beaulieu, MA, Villemure, JG, Olivier, A, Rasmussen, Th 2000Sturge-Weber syndrome. Indications and results of surgery in 20 patientsNeurology5514721479PubMedGoogle Scholar
  4. Roach, ES, Riela, AR, Chugani, HT 1994Sturge-Weber syndrome. Recommendations for surgeryJ Child Neurol9190192PubMedGoogle Scholar

Copyright information

© Springer-Verlag 2007

Authors and Affiliations

  • R. Ergün
    • 1
  • A. İ. Ökten
    • 2
  • Y. Gezercan
    • 2
  • A. R. Gezici
    • 1
  1. 1.Department of NeurosurgeryAbant İzzet Baysal UniversityBoluTurkey
  2. 2.Department of NeurosurgeryNumune HospitalAdanaTurkey

Personalised recommendations