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Acta Neurochirurgica

, Volume 148, Issue 12, pp 1297–1300 | Cite as

Hydrocephalus in Paget’s disease

  • A. V. Moiyadi
  • S. S. Praharaj
  • V. S. Pillai
  • B. A. Chandramouli
Short Illustrated Review

Summary

Neurological manifestations in Paget’s disease are rare. Hydrocephalus is infrequent, its etiology in Paget’s disease being multi-factorial. Surgical and anesthetic procedures may be challenging, requiring special precautions. We describe one such case and discuss these peculiarities. An elderly lady, diagnosed to have Paget’s disease presented with features of recent onset dementia, gait disturbances with urinary incontinence. Hydrocephalus secondary to posterior fossa crowding was present. A ventriculo-peritoneal shunt was inserted. Endotracheal intubation proved to be difficult. Modification of the surgical technique was required to ensure a safe procedure. She improved immediately following CSF diversion. Timely CSF diversion yields good results. Certain precautions during anesthesia and surgery can ensure a safe and uneventful peri-operative period.

Keywords: Paget’s disease, hydrocephalus, ventriculoperitoneal shunt, anesthesia, precautions. 

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Copyright information

© Springer-Verlag 2006

Authors and Affiliations

  • A. V. Moiyadi
    • 1
  • S. S. Praharaj
    • 1
  • V. S. Pillai
    • 1
  • B. A. Chandramouli
    • 1
  1. 1.Department of NeurosurgeryNational Institute of Mental Health and Neurosciences (NIMHANS)BangaloreIndia

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