Acta Neurochirurgica

, Volume 148, Issue 1, pp 83–87 | Cite as

Neuromuscular hamartoma of the trigeminal nerve in an adult

  • S. Tobias
  • C.-H. Kim
  • B. Sade
  • S. M. Staugaitis
  • J. H. Lee
Case Report

Summary

A 36-year-old female presented with a long-standing history of headache. Computed tomography scan and magnetic resonance imaging revealed an enhancing lesion occupying the right Meckel’s cave, enlarging the trigeminal ganglion and extending through the foramen ovale into the infratemporal fossa. A right frontotemporal extradural approach to the cavernous sinus was performed and a firm, pinkish lesion intermingled with nerve fibers enlarging the trigeminal ganglion and V3 branch was identified. Frozen section was suggestive of a neuromuscular hamartoma. The lesion was sub-totally resected to avoid injury to the motor branch.

Neuromuscular hamartoma should be included in the differential diagnosis of cavernous sinus and cranial nerve lesions in adults.

Keywords: Benign triton tumor; hamartoma; neuromuscular choristoma; schwannoma; trigeminal nerve. 

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Copyright information

© Springer-Verlag/Wien 2005

Authors and Affiliations

  • S. Tobias
    • 1
    • 2
  • C.-H. Kim
    • 1
    • 2
  • B. Sade
    • 1
    • 2
  • S. M. Staugaitis
    • 3
  • J. H. Lee
    • 1
    • 2
  1. 1.Department of NeurosurgeryCleveland Clinic FoundationClevelandUSA
  2. 2.Brain Tumor Institute, Cleveland Clinic FoundationClevelandUSA
  3. 3.Department of Anatomic PathologyCleveland Clinic FoundationClevelandUSA

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