Invasive intramedullary melanotic schwannoma: case report and review of the literature

  • Xing Cheng
  • Jiagang Liu
  • Jun Le
  • Siqing Huang
  • Haifeng chen
  • Chao You
Case Report

Abstract

Purpose

Melanotic schwannoma (MS) is rare, accounting for less than 1% of primary peripheral nerve sheath tumors, and most often occurs in the paraspinal nerve roots. Intramedullary MS is exceedingly rare, and to the best of our knowledge, only nine cases have been reported in literature.

Methods and Results

We present a 47-year-old male, who underwent excision of thoracic intraspinal space-occupying lesion 6 years ago, as the 10th known case to date of intradural intramedullary MS that had a more invasive growth pattern than those reported before, and we review the diagnosis, clinicopathologic features, treatment and prognosis of intramedullary MS.

Conclusions

Intramedullary MS’ behavior is unpredictable and can have an aggressive clinical course such as recurrence and metastasis.

Keywords

Intramedullary Melanotic Invasive Schwannoma 

Notes

Compliance with ethical standards

Conflict of interest

On behalf of all authors, the corresponding author states that there is no conflict of interest. The authors alone are responsible for the content and writing of this article.

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Copyright information

© Springer-Verlag GmbH Germany 2017

Authors and Affiliations

  • Xing Cheng
    • 1
    • 2
  • Jiagang Liu
    • 1
  • Jun Le
    • 3
  • Siqing Huang
    • 1
  • Haifeng chen
    • 1
  • Chao You
    • 1
  1. 1.Department of Neurosurgery, West China HospitalSichuan UniversityChengduPeople’s Republic of China
  2. 2.Department of NeurosurgeryChongqing Cancer HospitalChongqingPeople’s Republic of China
  3. 3.Department of NeurosurgeryYingtan People’s HospitalYingtanPeople’s Republic of China

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