Pediatric Nephrology

, Volume 21, Issue 11, pp 1765–1768 | Cite as

ACE inhibition can improve orthostatic proteinuria associated with nutcracker syndrome

Brief Report

Abstract

Left renal vein entrapment syndrome (nutcracker syndrome) was documented by magnetic resonance angiography (MRA) as a cause of orthostatic proteinuria in a 14-year-old girl female adolescent. Because of continuous proteinuria we performed a left renal biopsy which showed moderate mesangial hypercellularity. Her overt orthostatic proteinuria disappeared after a treatment of angiotensin-converting enzyme (ACE) inhibition. Nutcracker syndrome remains a rare but important cause of elevated protein excretion, which can induce mesangial changes and be improved by ACE inhibitor treatment.

Keywords

ACE inhibition Mesangial hypercellularity Nutcracker syndrome Orthostatic proteinuria 

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Copyright information

© IPNA 2006

Authors and Affiliations

  1. 1.Department of PediatricsChungbuk National University HospitalCheongju, ChungbukSouth Korea

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