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Pediatric Nephrology

, Volume 21, Issue 7, pp 1037–1040 | Cite as

Pseudo-Bartter syndrome in a pregnant mother and her fetus

  • Mikael Mathot
  • Pierre Maton
  • Elisabeth Henrion
  • Anne François-Adant
  • Arnaud Marguglio
  • Stéphanie Gaillez
  • Laure Collard
  • Jean-Paul LanghendriesEmail author
Brief Report

Abstract

Pseudo-Bartter syndrome presents the same clinical and biological characteristics as Bartter syndrome but without primary renal tubule abnormalities. We relate the case of a premature baby presenting at birth with severe hypokalemic metabolic alkalosis associated with hyponatremia and hypochloremia. Maternal blood at the time of delivery showed the same electrolyte perturbations. The baby’s mother had suffered from anorexia and vomiting during pregnancy. A few weeks after birth the baby’s blood abnormalities had almost returned to normal. Chloride depletion is at the origin of both maternal and fetal hypokalemic alkalosis.

Keywords

Pseudo-Bartter syndrome Eating disorders Hypokalemia Hypochloremia Metabolic alkalosis Placental electrolyte exchange Fetus Neonate 

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Copyright information

© IPNA 2006

Authors and Affiliations

  • Mikael Mathot
    • 1
  • Pierre Maton
    • 1
  • Elisabeth Henrion
    • 1
  • Anne François-Adant
    • 1
  • Arnaud Marguglio
    • 1
  • Stéphanie Gaillez
    • 1
  • Laure Collard
    • 2
  • Jean-Paul Langhendries
    • 1
    • 3
    Email author
  1. 1.CHC St Vincent Neonatology UnitRocourtBelgium
  2. 2.CHC St Vincent Pediatric NephrologyRocourtBelgium
  3. 3.NICUCHC-Site St VincentLiège-RocourtBelgium

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