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Dysphagia

, Volume 25, Issue 2, pp 127–138 | Cite as

Oropharyngolaryngeal Disorders in Scleroderma: Development and Validation of the SLS Scale

  • Chiara VitaliEmail author
  • Elisa Borghi
  • Arianna Napoletano
  • Francesca Polini
  • Monica Caronni
  • Paola Ammenti
  • Davide Cattaneo
Original Article

Abstract

Systemic sclerosis (SSc) is a multisystemic disorder characterized by functional and structural abnormalities of small blood vessels and fibrosis of the skin and internal organs. Eighty percent of subjects with SSc have orofacial manifestations. No tests for oral manifestations have been validated for this pathology, and in the literature there are few studies of speech therapy for subjects with SSc. These facts suggested the need for an exhaustive assessment of mouth mobility and muscle strength, and also of swallowing and voice, in order to plan a targeted and effective speech therapy. The Scleroderma Logopedic Scale (SLS) has been developed to assess disorders in five domains: Impairment, Swallow, Voice, Multifield, and Quality of Life. Perception of these disorders was assessed in 84 subjects with SSc and in 40 healthy subjects. After the first draft, a shorter form (39 items) was obtained after statistical analysis. This scale showed good discriminant and concurrent validity. Internal consistency was good: three of five subscales had a Cronbach α coefficient higher than 0.8. The test/retest coefficient for the total score was 0.94. Thirty-six percent of examined subjects showed moderate to severe oropharyngolaryngeal disorders. Swallowing disorders and impairment of mouth (e.g., decrease in mobility and strength) were the most commonly reported problems. Conversely, the change of voice due to the pathology was not perceived as a problem. Fifty-five percent of subjects reported a decreased level of quality of life.

Keywords

Scleroderma Oral disorders Swallow Voice Assessment Scale Deglutition Deglutition disorders 

Notes

Acknowledgment

This work was supported by the GILS (Gruppo Italiano Lotta alla Sclerodermia).

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Copyright information

© Springer Science+Business Media, LLC 2009

Authors and Affiliations

  • Chiara Vitali
    • 1
    • 3
    Email author
  • Elisa Borghi
    • 1
  • Arianna Napoletano
    • 1
  • Francesca Polini
    • 1
  • Monica Caronni
    • 2
  • Paola Ammenti
    • 1
  • Davide Cattaneo
    • 1
  1. 1.Department of NeurorehabilitationDon Gnocchi Foundation I.R.C.C.SMilanItaly
  2. 2.UOC Immunology Clinical Unit, I.R.C.C.S. Foundation, Ospedale Maggiore Policlinico Mangiagalli Regina ElenaMilanItaly
  3. 3.Servizio riabilitazione neurologica adulti (ext. 282)Don Gnocchi Foundation I.R.C.C.SMilanItaly

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