European Journal of Pediatrics

, Volume 170, Issue 10, pp 1305–1308 | Cite as

Gray hair and acrodermatitis enteropathica-like dermatitis: an unexpected presentation of cystic fibrosis

  • Buket Dalgic
  • Odul EgritasEmail author
Original Paper


Presentation of cystic fibrosis (CF) with an acrodermatitis enteropathica-like skin rash, anemia, and hypoproteinemia without pulmonary disease is rarely reported before. We describe an 11-month-old boy with rash and edema as the presenting signs of cystic fibrosis. The interesting additional finding in our patient was the graying hair after 3 months of age. A reversal of the gray hair was observed by pancreatic enzyme replacement therapy. In conclusion, acrodermatitis-like eruption and hypoproteinemia can be a presenting sign of CF. Graying hair has not been noticed so far as a sign of CF in these patients.


Cystic fibrosis Dermatitis Gray hair Acrodermatitis enteropathica-like dermatitis 


Disclosure of funding



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Copyright information

© Springer-Verlag 2011

Authors and Affiliations

  1. 1.Department of Pediatric GastroenterologyGazi University School of MedicineAnkaraTurkey

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