European Journal of Pediatrics

, Volume 169, Issue 5, pp 621–623 | Cite as

Congenital mitral regurgitation due to papillary muscle infarction: a case report and approach to evaluation

  • Zaheer Ahmad
  • Marcus Haw
  • Joseph J. VettukattilEmail author
Short Report


Congenital mitral regurgitation is relatively rare. It can be due to congenital malformation of the valve apparatus, associated structural heart defects, or results from myocardial dysfunction leading to deformation of the valve annulus. Hence, careful delineation of the pathologic processes involved in the mechanism is critical when evaluating patients presenting with congenital mitral valve regurgitation. Congenital anomalies of the coronary system are one of the serious associations, which needs prompt recognition and treatment to prevent fatal complications. We report a case of congenital atresia of left main coronary artery in an asymptomatic 8-month-old presenting with an incidental finding of mitral valvar regurgitation. Appropriate investigations and management lead to restoration of normal coronary blood flow and valve function. This particular case illustrates that congenital coronary anomalies may present in an otherwise asymptomatic child. It should be considered as one of the possible differential diagnosis in unexplained mitral regurgitation. Early recognition and prompt surgical treatment can radically modify the prognosis.


Left main coronary artery atresia Mitral regurgitation 


Conflicts of interest

The authors report that there are no disclosures or conflict of interest associated with this report.


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Copyright information

© Springer-Verlag 2009

Authors and Affiliations

  • Zaheer Ahmad
    • 1
  • Marcus Haw
    • 1
  • Joseph J. Vettukattil
    • 1
    Email author
  1. 1.Congenital Cardiac CentreSouthampton University Hospitals NHS TrustSouthamptonUK

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