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Virchows Archiv

, Volume 451, Issue 4, pp 835–838 | Cite as

Primary epithelioid sarcoma of the oesophagus

  • Francesca Maggiani
  • Maria Debiec-Rychter
  • Nadine Ectors
  • Antoon Lerut
  • Raf Sciot
Case Report

Abstract

Epithelioid sarcoma is a rare soft tissue tumour presenting two main variants: the ‘classical’ distal type and the more recently described proximal type. The latter is distinguished from the former by occurrence in elderly patients, more axial and deep location, prominent atypical and pleomorphic appearance and eventually aggressive clinical behaviour with poor outcome. To date, only few perivisceral epithelioid sarcomas have been described, and they are mainly related to the colon and bladder in pelvic and perineal sites. We report a hitherto undescribed epithelioid sarcoma of the distal oesophagus and discuss the relevance of molecular cytogenetics.

Keywords

Epithelioid sarcoma Extra-renal rhabdoid tumour Oesophagus Cytogenetics FISH 

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Copyright information

© Springer-Verlag 2007

Authors and Affiliations

  • Francesca Maggiani
    • 1
    • 2
  • Maria Debiec-Rychter
    • 3
  • Nadine Ectors
    • 2
  • Antoon Lerut
    • 4
  • Raf Sciot
    • 2
  1. 1.Medicina SperimentaleUniversità “La Sapienza” RomaRomeItaly
  2. 2.Department of Morphology and Molecular Pathology, University Hospital Sint RafaelCatholic University of LeuvenLeuvenBelgium
  3. 3.Department of Human Genetics, University Hospital GasthuisbergCatholic University of LeuvenLeuvenBelgium
  4. 4.Department of Thoracic Surgery, University Hospital GasthuisbergCatholic University of LeuvenLeuvenBelgium

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