Virchows Archiv

, Volume 446, Issue 5, pp 566–568 | Cite as

Congenital “clear cell sarcoma of the kidney”

Case Report


At 31 weeks gestation, a hydropic male fetus died in utero with metastatic disease from a renal clear cell sarcoma. The tumor had metastasized to para–aortic and mediastinal lymph nodes, lung, pleura, and liver, leading to superior vena cava obstruction and pulmonary hypoplasia. The pathologic findings and cytogenetic analysis of the fetus and tumor are presented. In addition, review of the literature reveals six other cases aged <6 months of age, including two extrarenal cases.


Clear cell sarcoma kidney Congenital Metastatic Cytogenetics 


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Copyright information

© Springer-Verlag 2005

Authors and Affiliations

  1. 1.Pathology DepartmentUniversity of Otago Medical SchoolDunedinNew Zealand

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