Polypoidal choroidal vasculopathy in a patient with angioid streaks secondary to pseudoxanthoma elasticum
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Pseudoxanthoma elasticum (PXE) is an inherited disorder characterized by the accumulation of calcified and fragmented elastin fibers in the skin, vascular walls, and Bruch’s membrane . Angioid streaks (AS), often complicated by secondary choroidal neovascularization (CNV), are the main ophthalmic manifestations of PXE.
Polypoidal choroidal vasculopathy (PCV) has been proposed to represent a variant of CNV . It now seems that alterations of the elastin matrix in vascular walls may be implicated in the occurrence of PCV.
We report a case of PCV in a patient diagnosed with PXE and formerly treated for subfoveal CNV secondary to AS.
KeywordsIntravitreal Injection Polypoidal Choroidal Vasculopathy Polypoidal Lesion Verteporfin Serous Retinal Detachment