Black diaphragm aniridia intraocular lens for aniridia and albinism

  • Victoria W. Y. Wong
  • Philip T. H. Lam
  • Timothy Y. Y. Lai
  • Dennis S. C. Lam
Case Report



Our aim was to assess the safety and efficacy of primary and secondary implantation of a black diaphragm aniridia intraocular lens (IOL) in patients that lacked a complete iris diaphragm.


This was a retrospective non-comparative study of six eyes in five patients with iris defects. The causes of such defects included congenital aniridia, traumatic aniridia, and oculocutaneous albinism. Three eyes underwent primary implantations of a black diaphragm IOL, and three eyes were given secondary implantations. The visual acuity, subjective severity of glare, postoperative anatomical outcome and any intraoperative or postoperative complications were reviewed.


The mean follow-up period was 20.6 months (range 3–29 months). All patients showed stable or improvement in best-corrected visual acuity postoperatively. Glare and photophobia had improved subjectively in all patients after implantation of the black diaphragm IOL. Intraoperative complication included one case of hyphaema and iris damage during insertion of the IOL. Postoperative complications included intraocular inflammation with choroidal detachment, secondary glaucoma, and persistent epithelial defect after surgery. None of the patients developed decentration of IOL after surgery.


The black diaphragm aniridia IOL is useful in the management of the condition in patients with iris deficiency including oculocutaneous albinism. Intraoperative and postoperative complications are not uncommon, and patients should be monitored carefully in the perioperative period.


  1. 1.
    Alger LG (1945) The cause and treatment of poor vision in aniridia. Am J Ophthalmol 28:730–735Google Scholar
  2. 2.
    Burk SE, Da Mata AP, Snyder ME, Cionni RJ, Cohen JS, Osher RH (2001) Prosthetic iris implantation for congenital, traumatic, or functional iris deficiencies. J Cataract Refract Surg 27:1732–1740PubMedGoogle Scholar
  3. 3.
    Burris TE, Holmes-Higgins DK, Silvestrini TA (1998) Lamellar intrastromal corneal tattoo for treating iris defects (artificial iris). Cornea 17:169–173CrossRefPubMedGoogle Scholar
  4. 4.
    Charles SJ, Green JS, Grant JW, Yates JR, Moore AT (1993) Clinical features of affected males with X linked ocular albinism. Br J Ophthalmol 77:222–227Google Scholar
  5. 5.
    Choyce P (1964) Intraocular lenses and implants. HK Lewis, LondonGoogle Scholar
  6. 6.
    Nishida K, Kinoshita S, Ohashi Y, Kuwayama Y, Yamamoto S (1995) Ocular surface abnormalities in aniridia. Am J Ophthalmol 120:368–375Google Scholar
  7. 7.
    Reinhard T, Engelhardt S, Sundmacher R (2000) Black diaphragm aniridia intraocular lens for congenital aniridia: long-term follow-up. J Cataract Refract Surg 26:375–381PubMedGoogle Scholar
  8. 8.
    Sundmacher R, Reinhard T, Althaus C (1994) Black diaphragm intraocular lens in congenital aniridia. Eur J Ophthalmol 3:197–201Google Scholar
  9. 9.
    Sundmacher R, Reinhard T, Althaus C (1994) Black-diaphragm intraocular lens for correction of aniridia. Ophthalmic Surg 25:180–185PubMedGoogle Scholar
  10. 10.
    Thompson CG, Fawzy K, Bryce IG, Noble BA (1999) Implantation of a black diaphragm intraocular lens for traumatic aniridia. J Cataract Refract Surg 25:808–813PubMedGoogle Scholar

Copyright information

© Springer-Verlag 2004

Authors and Affiliations

  • Victoria W. Y. Wong
    • 1
    • 2
  • Philip T. H. Lam
    • 1
    • 2
  • Timothy Y. Y. Lai
    • 1
    • 2
  • Dennis S. C. Lam
    • 1
  1. 1.Department of Ophthalmology and Visual Sciences, Hong Kong Eye HospitalThe Chinese University of Hong KongHong KongPeople’s Republic of China
  2. 2.Hospital Authority Ophthalmic ServiceHong Kong Eye HospitalKowloonPeople’s Republic of China

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