Journal of Neurology

, 256:176 | Cite as

The management of amyotrophic lateral sclerosis

  • J. PhukanEmail author
  • O. Hardiman


The terms amyotrophic lateral sclerosis (ALS) or motor neuron disease (MND) refer to a condition characterized by motor system degeneration with relative preservation of other pathways. Although there have been advances in symptomatic treatment, ALS remains an incurable condition. Advances in ALS management prolong survival but simultaneously raise challenging ethical dilemmas for physicians, patients and their families. Here, we review current practice in the management of ALS including pharmacological treatment, nutritional management, respiratory care, and evolving strategies in the management of cognitive impairment.

Key words

amyotrophic lateral sclerosis motor neurone disease management 


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Copyright information

© Steinkopff-Verlag 2009

Authors and Affiliations

  1. 1.Dept. of NeurologyBeaumont HospitalDublin 9Ireland
  2. 2.Trinity College Institute of NeuroscienceDublin 9Ireland

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