Interstitial Lung Disease in a Child with Antisynthetase Syndrome
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Antisynthetase Syndrome is associated with interstitial lung disease in adult patients, but this has not been described in children.
Materials and methods
A 13-year-old with interstitial lung disease due to Antisynthetase Syndrome and pulmonary arterial hypertension underwent emergent bilateral lung transplantation after a rapid clinical decline.
We present the clinical, radiographic, and histological findings of a child with interstitial lung disease due to Antisynthetase Syndrome.
KeywordsAntisynthetase syndrome Anti-Jo-1 antibody Child Interstitial lung disease
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