European Archives of Oto-Rhino-Laryngology

, Volume 270, Issue 5, pp 1757–1761 | Cite as

Cochlear implantation in a child with posttraumatic single-sided deafness

  • Stefan K. Plontke
  • Cornelia Heider
  • Sabrina Koesling
  • Sören Hess
  • Lars Bieseke
  • Gerrit Goetze
  • Torsten Rahne
Case Report

Abstract

Cochlear implantation has become a standard therapy for children with bilateral profound hearing loss, resulting in substantial and sustainable benefits for the development of expressive and receptive and expressive language skills and cognition. During the last few years, audiologic and otologic criteria for cochlear implantation have been expanded. Recently, patients with profound single-sided deafness with or without tinnitus have received cochlear implants despite normal to near-normal hearing on the contralateral side. This indication, however, has thus far been restricted to adult patients. Although it is known that unilateral hearing has an impact on social-emotional development in children, otologic surgeons have been reluctant to treat children with single-sided deafness with a cochlear implant. We report here on a case of successful cochlear implantation in an 8-year-old boy with acute single-sided deafness due to a lateral skull-base fracture, after an MRI showed signs of imminent fibrosis of the inner ear with possible prevention of cochlear implantation at a later stage. There was normal hearing in the contralateral ear. The child showed rapid development of speech discrimination in the implanted ear, improvements in sound localization and speech perception in noise, and a high degree of patient satisfaction. This experience may encourage using this therapeutic approach in children with chronic profound single-sided deafness.

Keywords

Child Cochlear implant Hearing loss Single-sided deafness (SSD) Temporal bone fracture Unilateral hearing loss (UHL) 

Abbreviations

ADE

Angle-detection error

BAHA

Bone-anchored hearing aids

CI

Cochlear implant

CISS

Constructive interference steady-state sequence

CROS

Contralateral routing of sound

CT

Computed tomography

dB

Decibel

HL

Hearing level

MRI

Magnetic resonance imaging

nHL

Normalized hearing level

OLSA

Oldenbourg sentence test

SDS

Speech discrimination score

SPL

Sound pressure level

SSD

Single-sided deafness

SRT

Speech reception threshold

UHL

Unilateral hearing loss

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Copyright information

© Springer-Verlag Berlin Heidelberg 2013

Authors and Affiliations

  • Stefan K. Plontke
    • 1
  • Cornelia Heider
    • 1
  • Sabrina Koesling
    • 2
  • Sören Hess
    • 3
  • Lars Bieseke
    • 1
  • Gerrit Goetze
    • 1
  • Torsten Rahne
    • 1
  1. 1.Department of Otorhinolaryngology, Head and Neck SurgeryHearing and Implant Center Halle, University of Halle-WittenbergHalle (Saale)Germany
  2. 2.Department of Diagnostic RadiologyUniversity of Halle-WittenbergHalle (Saale)Germany
  3. 3.Department of PediatricsUniversity of Halle-WittenbergHalle (Saale)Germany

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