European Archives of Oto-Rhino-Laryngology

, Volume 266, Issue 4, pp 501–506 | Cite as

Congenital auditory meatal atresia: a numerical review

  • Mohammad Abdel-Azim El-Begermy
  • Ossama Ibrahim Mansour
  • Aly Mohammad Nagy El-Makhzangy
  • Tamer Saleh El-Gindy
Otology

Abstract

Congenital auditory meatal atresia (CAMA) is an uncommonly encountered disorder. Though a rare condition, CAMA poses multiple problems for affected children. Recent management of CAMA in developed countries rests on osseo-integrated prostheses and bone-anchored hearing aids. The situation is different in developing countries where aesthetic and otologic surgeries are the available lines of management. Surgical management of CAMA has been staged into reconstructive surgery for auricular deformity followed by external and middle ear reconstruction either via anterior or transmastoid approaches. Multiple case series describing the outcomes and complications of both approaches have been published, but no authors have attempted to compare either. We have attempted to compare the outcomes and complications of both approaches by analyzing published medical articles concerning surgical management of CAMA identified by searching the Medline database using “congenital aural atresia” and “external auditory canal atresia” as keywords. A total of 923 ears were reported by 13 articles included in this study. The transmastoid approach is shown, by multiple linear regression, to have better postoperative hearing gain and less likely restenosis.

Keywords

Congenital Auditory Aural Atresia Anterior approach Transmastoid approach Complications Outcomes Multiple linear regression 

References

  1. 1.
    Altmann F (1955) Congenital atresia of the ear in man and animals. Ann Otol Rhinol Laryngol 64:824–858PubMedGoogle Scholar
  2. 2.
    Bauer GP, Wiet RJ, Zappia JJ (1994) Congenital aural atresia. Laryngoscope 104:1219–1224PubMedGoogle Scholar
  3. 3.
    Caversaccio M, Romualdez J, Baechler R, Nolte LP, Komps M, Hausler R (2003) Valuable use of computer-aided surgery in congenital bony aural atresia. J Laryngol Otol 117:241–248PubMedGoogle Scholar
  4. 4.
    Chang SO, Min YG, Kim CS, Koh TY (1994) Surgical management of congenital aural atresia. Laryngoscope 104:606–611PubMedCrossRefGoogle Scholar
  5. 5.
    Chang SO, Jeon SJ, Jeong HS, Kim CS (2002) Prevention of postoperative meatal stenosis with anteriorly and inferiorly based periosteal flap in congenital aural atresia surgery. Otol Neurotol 23:25–28PubMedCrossRefGoogle Scholar
  6. 6.
    Chang SO, Choi BY, Hur DG (2006) Analysis of the long-term hearing results after the surgical repair of aural atresia. Laryngoscope 116:1835–1841PubMedCrossRefGoogle Scholar
  7. 7.
    De La Cruz A, Teufert KB (2003) Congenital aural atresia surgery: long-term results. Otolaryngol Head Neck Surg 131:263–270CrossRefGoogle Scholar
  8. 8.
    De La Cruz A, Linthicum HF, Luxford W (1985) Congenital atresia of the external auditory canal. Laryngoscope 95:421–427CrossRefGoogle Scholar
  9. 9.
    Granström G, Bergström K, Tjellström A (1993) The bone-anchored hearing aid and bone-anchored epithesis for congenital ear malformations. Otolaryngol Head Neck Surg 109:46–53PubMedGoogle Scholar
  10. 10.
    Jahrsdoerfer RA (2003) Surgery for congenital aural atresia. In: Glasscock ME, Gulya AJ (eds) Glasscock-Shambaugh surgery of the ear, 5th edn. BC Decker, Hamilton, pp 389–399Google Scholar
  11. 11.
    Jahrsdoerfer RA, Yeakley JW, Aguilar EA, Cole RR, Gray LC (1992) Grading system for the selection of patients with congenital aural atresia. Am J Otol 13:6–12PubMedGoogle Scholar
  12. 12.
    Lambert PR (1988) Major congenital ear malformations: surgical management and results. Ann Otol Rhinol Laryngol 97:641–649PubMedGoogle Scholar
  13. 13.
    Lambert PR (1998) Congenital aural atresia: stability of surgical results. Laryngoscope 108:1801–1805PubMedCrossRefGoogle Scholar
  14. 14.
    Marres EH, Cremers CW (1985) Surgical treatment of congenital aural atresia. Am J Otol 6:247–249PubMedGoogle Scholar
  15. 15.
    Minatogawa T, Nishimura Y, Inamori T, Kumoi T (1989) Results of tympanoplasty for congenital aural atresia and stenosis with special reference to fascia and homograft material of the tympanic membrane. Laryngoscope 99:632–638PubMedCrossRefGoogle Scholar
  16. 16.
    Nishizaki K, Masuda YU, Karita K (1999) Surgical management and its postoperative complications in congenital aural atresia. Acta Otolaryngol 540(Suppl):42–44Google Scholar
  17. 17.
    Petrie A, Bulman JS, Osborn JF (2002) Further statistics in dentistry: Part 6: multiple linear regression. Br Dent J 193:675–682PubMedCrossRefGoogle Scholar
  18. 18.
    Powell RH, Burrell SP, Cooper HR, Proops DW (1996) The Birmingham bone anchored hearing aid programme: paediatric experience and results. J Laryngol Otol 21(Suppl):21–29Google Scholar
  19. 19.
    Schuknecht HF (1989) Congenital aural atresia. Laryngoscope 99:908–917PubMedCrossRefGoogle Scholar
  20. 20.
    Shih L, Crabtree JA (1993) Long-term surgical results for congenital aural atresia. Laryngoscope 103:1097–1102PubMedCrossRefGoogle Scholar
  21. 21.
    Smillie KW (1966) An introduction to regression and correlation. Academic, LondonGoogle Scholar
  22. 22.
    Teufert KB, De La Cruz A (2004) Advances in congenital aural atresia surgery: effects on outcome. Otolaryngol Head Neck Surg 131:263–270PubMedCrossRefGoogle Scholar
  23. 23.
    Thacker SB (1988) Meta-analysis. A quantitative approach to research integration. JAMA 259:1685–1689PubMedCrossRefGoogle Scholar
  24. 24.
    Veltmann JA, Jonkers Y, Nuijten I, Janssen I, van der Vliet W, Huys E, Vermeesch J, Van Buggenhout G, Fryns JP, Admiraal R, Terhal P, Lacombe D, van Kessel AG, Smeets D, Schoenmakers EFPM, van Ravenswaaij-Arts CM (2003) Definition of a critical region on chromosome 18 for congenital aural atresia by array CGH. Am J Hum Genet 72:1578–1584CrossRefGoogle Scholar

Copyright information

© Springer-Verlag 2008

Authors and Affiliations

  • Mohammad Abdel-Azim El-Begermy
    • 1
  • Ossama Ibrahim Mansour
    • 1
  • Aly Mohammad Nagy El-Makhzangy
    • 1
  • Tamer Saleh El-Gindy
    • 2
  1. 1.Department of Otorhinolaryngology, Faculty of MedicineAin Shams UniversityCairoEgypt
  2. 2.Department of OtorhinolaryngologyShirbeen General Hospital (MOH)MansouraEgypt

Personalised recommendations