Archives of Gynecology and Obstetrics

, Volume 277, Issue 6, pp 483–487 | Cite as

Aggressive angiomyxoma of the vulva: a case report and review of literature

  • Inge Dierickx
  • Karen Deraedt
  • Willy Poppe
  • Jasper Verguts
Review Article
First Online:
Received:
Accepted:

Abstract

Background

Aggressive angiomyxoma (AA) is a rare vulvovaginal mesenchymal neoplasm with a marked tendency to local recurrence but which usually does not metastasize.

Case report

We describe a case of AA in the left labium majus pudendi in a 47-year-old woman who underwent incomplete surgical excision. Follow-up 2 years later revealed no recurrence.

Conclusion

In the past, most authors advocated wide excision even if genitourinary and digestive tract resection were necessary. These days, a less radical surgery is recommended, but the significance of hormonal treatment and/or radiation therapy is not clear yet. Further investigation is necessary.

Keywords

Aggressive angiomyxoma Vulva Treatment 
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Copyright information

© Springer-Verlag 2008

Authors and Affiliations

  • Inge Dierickx
    • 1
  • Karen Deraedt
    • 2
  • Willy Poppe
    • 1
  • Jasper Verguts
    • 1
    • 3
  1. 1.Department of Obstetrics and GynaecologyKatholieke Universiteit LeuvenLeuvenBelgium
  2. 2.Department of PathologyKatholieke Universiteit LeuvenLeuvenBelgium
  3. 3.Department of Obstetrics and GynaecologyUniversity Hospital GasthuisbergLeuvenBelgium

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