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Archives of Orthopaedic and Trauma Surgery

, Volume 122, Issue 2, pp 120–122 | Cite as

Myelopathy due to scoliosis with vertebral hypertrophy in Klippel-Trenaunay-Weber syndrome

  • Yasuhisa Arai
  • Tatsuya Takagi
  • Torahiro Matsuda
  • Hisashi Kurosawa
Current Problem Case

Abstract.

We describe a 37-year-old man complaining of right back pain and gait disturbance. He had a big soft tumor on his right back, hemihypertrophy of the right lower extremity, and right thoracic scoliosis. We diagnosed Klippel-Trenaunay-Weber syndrome based on the pathological findings of the soft tumor. Computed tomography (CT) scan revealed severe spinal stenosis due to a hypertrophic vertebral body and facet joint at T7. Treatment by decompression of hypertrophic bone led to complete neurological recovery. To our knowledge, no case has been reported of Klippel-Trenaunay-Weber syndrome with myelopathy which originated from thoracic scoliosis with a hypertrophic facet joint and vertebral body. We suggest that the cause of myelopathy in Klippel-Trenaunay-Weber syndrome originated not only from arteriovenous fistula, medullary angioma, and extradural hemangioma but also vertebral hypertrophy with scoliosis.

Klippel-Trenaunay-Weber syndrome Myelopathy Vertebral hypertrophy 

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Copyright information

© Springer-Verlag 2001

Authors and Affiliations

  • Yasuhisa Arai
    • 1
  • Tatsuya Takagi
    • 1
  • Torahiro Matsuda
    • 1
  • Hisashi Kurosawa
    • 1
  1. 1.Department of Orthopaedic Surgery, Juntendo University, School of Medicine, 2-1-1, Hongo, Bunkyo-ku, Tokyo 113-8421, Japan

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