Pediatric Surgery International

, Volume 34, Issue 1, pp 113–116 | Cite as

The challenges of closing an ileostomy in patients with total intestinal aganglionosis after small bowel transplant

  • Fereshteh Salimi Jazi
  • Tiffany J. Sinclair
  • Chad M. Thorson
  • Ricardo Castillo
  • Andrew C. Bonham
  • Carlos O. Esquivel
  • Matias BruzoniEmail author
Case Report


We present the case of a 14-year-old male with a history of small bowel transplantation for long segment Hirschsprung’s disease who underwent Duhamel ileorectal pull-through procedure. In post-transplant, the patient had no restrictions and was not TPN-dependent. To improve his quality of life, he and his family were interested in closing the ileostomy and undergoing pull-through surgery. The complexity of the case includes the presence of an aganglionic rectal segment—a short root of the mesentery due to the small bowel transplant—and significant immunosuppression. At the moment, he is continent, doing well, and has not had any remarkable complications.


Total intestinal aganglionosis Small bowel transplantation Hirschsprung’s disease 


Compliance with ethical standards

Conflict of interest

The authors declare that they have no conflicts of interest.

Ethical approval

All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

Informed consent

Informed consent was obtained from all individual participants included in the study.


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Copyright information

© Springer-Verlag GmbH Germany, part of Springer Nature 2017

Authors and Affiliations

  • Fereshteh Salimi Jazi
    • 1
  • Tiffany J. Sinclair
    • 2
  • Chad M. Thorson
    • 1
  • Ricardo Castillo
    • 3
  • Andrew C. Bonham
    • 4
  • Carlos O. Esquivel
    • 4
  • Matias Bruzoni
    • 1
    Email author
  1. 1.Division of Pediatric Surgery, Department of SurgeryLucile Packard Children’s at Stanford University School of MedicineStanfordUSA
  2. 2.Department of SurgeryStanford University School of MedicineStanfordUSA
  3. 3.Division of GastroenterologyLucile Packard Children’s at Stanford University School of MedicineStanfordUSA
  4. 4.Division of Transplant SurgeryStanford University School of MedicineStanfordUSA

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