We present a 7-month-old male with Pompe’s disease with respiratory failure requiring extracorporeal membrane oxygenation that received enzyme replacement therapy. There are no published cases of the use of extracorporeal membrane oxygenation in a patient with Pompe’s disease, or the use of enzyme replacement therapy in the setting of acute respiratory failure.
Pompe’s disease Respiratory syncytial virus Glycogen storage disease type II Extracorporeal membrane oxygenation (ECMO) Acid alpha-glucosidase
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