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Pediatric Surgery International

, Volume 30, Issue 5, pp 553–555 | Cite as

Initiation of ECMO for ventilator-dependent respiratory failure in an infant with Pompe’s

  • Christina RiojasEmail author
  • Walter Pipkin
Case Report
  • 209 Downloads

Abstract

We present a 7-month-old male with Pompe’s disease with respiratory failure requiring extracorporeal membrane oxygenation that received enzyme replacement therapy. There are no published cases of the use of extracorporeal membrane oxygenation in a patient with Pompe’s disease, or the use of enzyme replacement therapy in the setting of acute respiratory failure.

Keywords

Pompe’s disease Respiratory syncytial virus Glycogen storage disease type II Extracorporeal membrane oxygenation (ECMO) Acid alpha-glucosidase 

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Copyright information

© Springer-Verlag Berlin Heidelberg 2014

Authors and Affiliations

  1. 1.General Surgery DepartmentDwight David Eisenhower Army Medical CenterAugustaUSA
  2. 2.Children’s Hospital of GeorgiaAugustaUSA

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